Anti DYSF pAb (ATL-HPA017071 w/enhanced validation)

Atlas Antibodies

SKU:
ATL-HPA017071-25
  • Immunohistochemistry analysis in human skeletal muscle and skin tissues using HPA017071 antibody. Corresponding DYSF RNA-seq data are presented for the same tissues.
  • Immunofluorescent staining of human cell line RH-30 shows localization to plasma membrane & microtubule organizing center.
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Protein Description: dysferlin
Gene Name: DYSF
Alternative Gene Name: FER1L1, LGMD2B
Isotype: IgG
Interspecies mouse/rat: ENSMUSG00000033788: 96%, ENSRNOG00000032788: 96%
Entrez Gene ID: 8291
Uniprot ID: O75923
Buffer: 40% glycerol and PBS (pH 7.2). 0.02% sodium azide is added as preservative.
Storage Temperature: Store at +4°C for short term storage. Long time storage is recommended at -20°C.

Product Specifications
Application ICC, IHC
Reactivity Human
Clonality Polyclonal
Host Rabbit
Immunogen IVVELYDHDTYGADEFMGRCICQPSLERMPRLAWFPLTRGSQPSGELLASFELIQREKPAIHHIPGFEVQETSRILDESEDTDLPYPPPQREANIYMVPQNIKPALQRTAIEILAWG
Gene Sequence IVVELYDHDTYGADEFMGRCICQPSLERMPRLAWFPLTRGSQPSGELLASFELIQREKPAIHHIPGFEVQETSRILDESEDTDLPYPPPQREANIYMVPQNIKPALQRTAIEILAWG
Gene ID - Mouse ENSMUSG00000033788
Gene ID - Rat ENSRNOG00000032788
Buffer 40% glycerol and PBS (pH 7.2). 0.02% sodium azide is added as preservative.


Documents & Links for Anti DYSF pAb (ATL-HPA017071 w/enhanced validation)
Datasheet Anti DYSF pAb (ATL-HPA017071 w/enhanced validation) Datasheet (External Link)
Vendor Page Anti DYSF pAb (ATL-HPA017071 w/enhanced validation) at Atlas Antibodies

Documents & Links for Anti DYSF pAb (ATL-HPA017071 w/enhanced validation)
Datasheet Anti DYSF pAb (ATL-HPA017071 w/enhanced validation) Datasheet (External Link)
Vendor Page Anti DYSF pAb (ATL-HPA017071 w/enhanced validation)



Citations for Anti DYSF pAb (ATL-HPA017071 w/enhanced validation) – 1 Found
Ono, Hiroya; Suzuki, Naoki; Kanno, Shin-Ichiro; Kawahara, Genri; Izumi, Rumiko; Takahashi, Toshiaki; Kitajima, Yasuo; Osana, Shion; Nakamura, Naoko; Akiyama, Tetsuya; Ikeda, Kensuke; Shijo, Tomomi; Mitsuzawa, Shio; Nagatomi, Ryoichi; Araki, Nobukazu; Yasui, Akira; Warita, Hitoshi; Hayashi, Yukiko K; Miyake, Katsuya; Aoki, Masashi. AMPK Complex Activation Promotes Sarcolemmal Repair in Dysferlinopathy. Molecular Therapy : The Journal Of The American Society Of Gene Therapy. 2020;28(4):1133-1153.  PubMed