Anti BCS1L pAb (ATL-HPA037701)

Atlas Antibodies

SKU:
ATL-HPA037701-25
  • Immunohistochemical staining of human liver shows strong cytoplasmic positivity in hepatocytes.
  • Lane 1: Marker [kDa] 250, 130, 95, 72, 55, 36, 28, 17, 10<br/>Lane 2: Human cell line RT-4<br/>Lane 3: Human cell line U-251MG sp
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Protein Description: BC1 (ubiquinol-cytochrome c reductase) synthesis-like
Gene Name: BCS1L
Alternative Gene Name: BCS, BJS, h-BCS, Hs.6719
Isotype: IgG
Interspecies mouse/rat: ENSMUSG00000026172: 98%, ENSRNOG00000016754: 100%
Entrez Gene ID: 617
Uniprot ID: Q9Y276
Buffer: 40% glycerol and PBS (pH 7.2). 0.02% sodium azide is added as preservative.
Storage Temperature: Store at +4°C for short term storage. Long time storage is recommended at -20°C.

Product Specifications
Application WB, IHC
Reactivity Human
Clonality Polyclonal
Host Rabbit
Immunogen LEHSICLLSLTDSSLSDDRLNHLLSVAPQQSLVLLEDVDAAFLSRDLAVENPVKYQGLGRLTFSGLLNALDGVASTEARIVFMTTNH
Gene Sequence LEHSICLLSLTDSSLSDDRLNHLLSVAPQQSLVLLEDVDAAFLSRDLAVENPVKYQGLGRLTFSGLLNALDGVASTEARIVFMTTNH
Gene ID - Mouse ENSMUSG00000026172
Gene ID - Rat ENSRNOG00000016754
Buffer 40% glycerol and PBS (pH 7.2). 0.02% sodium azide is added as preservative.


Documents & Links for Anti BCS1L pAb (ATL-HPA037701)
Datasheet Anti BCS1L pAb (ATL-HPA037701) Datasheet (External Link)
Vendor Page Anti BCS1L pAb (ATL-HPA037701) at Atlas Antibodies

Documents & Links for Anti BCS1L pAb (ATL-HPA037701)
Datasheet Anti BCS1L pAb (ATL-HPA037701) Datasheet (External Link)
Vendor Page Anti BCS1L pAb (ATL-HPA037701)



Citations for Anti BCS1L pAb (ATL-HPA037701) – 1 Found
Tegelberg, Saara; Tomašić, Nikica; Kallijärvi, Jukka; Purhonen, Janne; Elmér, Eskil; Lindberg, Eva; Nord, David Gisselsson; Soller, Maria; Lesko, Nicole; Wedell, Anna; Bruhn, Helene; Freyer, Christoph; Stranneheim, Henrik; Wibom, Rolf; Nennesmo, Inger; Wredenberg, Anna; Eklund, Erik A; Fellman, Vineta. Respiratory chain complex III deficiency due to mutated BCS1L: a novel phenotype with encephalomyopathy, partially phenocopied in a Bcs1l mutant mouse model. Orphanet Journal Of Rare Diseases. 2017;12(1):73.  PubMed